PubMed: | Chemical compositional, biological, and safety studies of a novel maple syrup derived extract for nutraceutical applications. |
PubMed: | Nonnutritive sweeteners are not supernormal stimuli. |
PubMed: | Nutrition management guideline for maple syrup urine disease: an evidence- and consensus-based approach. |
PubMed: | Preservation of high phenylalanine ammonia lyase activities in roots of Japanese Striped corn: a potential oral therapeutic to treat phenylketonuria. |
PubMed: | Maple Syrup Urine Disease Complicated with Kyphoscoliosis and Myelopathy. |
PubMed: | [The use of low-calorie sweeteners]. |
PubMed: | Adipose transplant for inborn errors of branched chain amino acid metabolism in mice. |
PubMed: | Drosophila miR-277 controls branched-chain amino acid catabolism and affects lifespan. |
PubMed: | Potential of fluorescence spectroscopy for the characterisation of maple syrup flavours. |
PubMed: | Treatment of acute decompensation of maple syrup urine disease in adult patients with a new parenteral amino-acid mixture. |
PubMed: | Maple polyphenols, ginnalins A-C, induce S- and G2/M-cell cycle arrest in colon and breast cancer cells mediated by decreasing cyclins A and D1 levels. |
PubMed: | Risk assessment and risk management at the Canadian Food Inspection Agency (CFIA): a perspective on the monitoring of foods for chemical residues. |
PubMed: | Maple sap predominant microbial contaminants are correlated with the physicochemical and sensorial properties of maple syrup. |
PubMed: | Analysis of human male armpit sweat after fenugreek ingestion: Characterisation of odour active compounds by gas chromatography coupled to mass spectrometry and olfactometry. |
PubMed: | Further investigation into maple syrup yields 3 new lignans, a new phenylpropanoid, and 26 other phytochemicals. |
PubMed: | Comparison of nonfried apple snacks with commercially available fried snacks. |
PubMed: | Maple syrup phytochemicals include lignans, coumarins, a stilbene, and other previously unreported antioxidant phenolic compounds. |
PubMed: | Antioxidant activity, inhibition of nitric oxide overproduction, and in vitro antiproliferative effect of maple sap and syrup from Acer saccharum. |
PubMed: | Changing carbon isotope ratio of atmospheric carbon dioxide: implications for food authentication. |
PubMed: | Classical maple syrup urine disease and brain development: principles of management and formula design. |
PubMed: | Maple syrup-production, composition, chemistry, and sensory characteristics. |
PubMed: | Total antioxidant content of alternatives to refined sugar. |
PubMed: | Improved detection of sugar addition to maple syrup using malic acid as internal standard and in 13C isotope ratio mass spectrometry (IRMS). |
PubMed: | The generation of formaldehyde in cigarettes--Overview and recent experiments. |
PubMed: | A new protein substitute for adolescents and adults with maple syrup urine disease (MSUD). |
PubMed: | Branched-chain amino acids and brain function. |
PubMed: | Legal strategies to address the misrepresentation of Vermont maple syrup. |
PubMed: | Microwave processing of maple sap to maple syrup and maple syrup products. |
PubMed: | Spectrofluorimetric determination of formaldehyde in maple syrup. |
PubMed: | Utility of hemodialysis in maple syrup urine disease. |
PubMed: | Detection of added beet or cane sugar in maple syrup by the site-specific deuterium nuclear magnetic resonance (SNIF-NMR) method: collaborative study. |
PubMed: | Whole-body L-leucine oxidation in patients with variant form of maple syrup urine disease. |
PubMed: | Limitations in the use of ozone to disinfect maple sap. |
PubMed: | Diagnosis of inborn errors of metabolism. |
PubMed: | 4,5-dimethyl-3-hydroxy-2[5H]-furanone (sotolone)--the odour of maple syrup urine disease. |
PubMed: | Peculiar odor of traditional food and maple syrup urine disease. |
PubMed: | Sugar nucleotide concentrations in red blood cells of patients on protein- and lactose-limited diets: effect of galactose supplementation. |
PubMed: | Making maple syrup: hazardous a vocational ingestion of raw sap in a patient with nut and tree pollen sensitivity. |
PubMed: | [Lists of food exchanges for use in phenylketonuria and maple-syrup urine disease]. |
PubMed: | [Methodology of care for children with phenylketonuria and maple-syrup urine disease]. |
PubMed: | Acrodermatitis enteropathica-like syndrome secondary to isoleucine deficiency during treatment of maple syrup urine disease. |
PubMed: | Nutrient intakes of adolescents with phenylketonuria and infants and children with maple syrup urine disease on semisynthetic diets. |
PubMed: | Sample preparation bias in carbon stable isotope ratio analysis of fruit juices and sweeteners. |
PubMed: | Inherited enzyme deficiencies in livestock. |
PubMed: | Dietary management of inborn errors of amino acid metabolism with protein-modified diets. |
PubMed: | High levels of dietary amino and branched-chain alpha-keto acids alter plasma and brain amino acid concentrations in rats. |
PubMed: | Selenium in pediatric nutrition. |
PubMed: | Analysis of selenium content in commercial dietetic products. |
PubMed: | Evaluation of branched-chain amino acid intake in children with maple syrup urine disease and methylmalonic aciduria. |
PubMed: | Gas chromatographic determination of formaldehyde in maple syrup as 2,4-dinitrophenylhydrazone derivative. |
PubMed: | [Isolated isoleucine deficiency in diet therapy of a case of maple syrup urine disease]. |
PubMed: | Azetidine-2-carboxylic acid contaminated dietary proline as a cause of urinary excretion of 4-amino-2-(S-cysteinyl)butyric acid in patients on oral treatment with a synthetic diet. |
PubMed: | Prospective study of maple-syrup-urine disease for the first four days of life. |
PubMed: | Acidosis associated with dietotherapy of maple syrup urine disease. |
PubMed: | Dietary management of maple-sirup-urine disease: extension of equivalency systems. |
PubMed: | Dietary restriction in inborn errors of amino acid metabolism. |
PubMed: | Selenium concentration and glutathione peroxidase activity in blood of New Zealand infants and children. |
PubMed: | Maple syrup urine disease: emergency treatment of the neonate. |
PubMed: | Management of maple syrup urine disease in Canada. Committee for improvement of Hereditary Disease Management. |
PubMed: | Dietary treatment of maple sirup urine disease (branched-chain ketoaciduria). |
PubMed: | The dietary therapy of inherited metabolic disease. |
PubMed: | Mineral and trace-metal balances in children receiving normal and synthetic diets. |
PubMed: | Leucine equivalency system in managing branched chain ketoaciduria. |
PubMed: | Folic acid deficiency secondary to a diet for maple syrup urine disease. |